Multifocal fibrous Dysplasia with enchondroma-like areas (Fibrocartilaginous Dysplasia)
نویسندگان
چکیده
Fibrocartilaginous dysplasia is a variant of fibrous dysplasia showing extensive cartilaginous differentiation (enchondroma-like areas). The amount of cartilage varies from case to case. This has been reported more commonly in polyostotic disease. We present a 19 year old boy who presented with multifocal osteolytic lesions involving right femoral neck and lower end of left fibula. Curettage of the lesions showed translucent cartilaginous fragments. Microscopy revealed a cartilaginous (70%) and fibro-osseous (30%) component; the former showed focally increased cellularity while the latter showed features of fibrous dysplasia.
منابع مشابه
Fibrocartilaginous dysplasia: a variant of fibrous dysplasia.
Eight cases of fibrous dysplasia having enchondroma-like areas (fibrocartilaginous dysplasia) are reported. Four patients were male, four were female. The patients' ages ranged from 8 to 18 years (mean = 11.3 years). In seven cases, the lesions were located at the proximal femur while one was at the tibial diaphysis. Histologically, large, well-defined, sharply demarcated islands of hyaline car...
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